Based on the comments of fellow PRP patients and caregivers, dermatologists seem reticent to go beyond a simple diagnosis. We are told Adult Onset PRP or Juvenile Onset PRP. The age of onset makes that an easy call. As PRP patients and caregivers, we want to know where we fit it.
Atypical Adult Onset
With adults, the “estimated” rarity of Atypical Adult Onset, Type 2 (5 out of 100) means that Classical Adult Onset, Type 1 is almost assumed. Moreover, the treatment protocol is the same for Type 1 and Type 2.
Atypical Juvenile Onset
In contrast, parents of a child diagnosed with PRP want to know that their child does not have Atypical Juvenile Onset, Type 5, the most chronic version of Juvenile Onset PRP (5 out of 100 PRP patients).
HIV-associated PRP
The most rare form of PRP is Type 6. A diagnosis of HIV-associated PRP simply means that treatment options will be limited and far more challenging.
For those with Atypical Adult Onset (Type 2) and Atypical Juvenile Onset (Type 5), the PRP journey does not have remission as a final destination. Rather, the objective is long-term management of symptoms.
http://www.dermnetnz.org/topics/pityriasis-rubra-pilaris
